ⓘ Aminoadipate-semialdehyde dehydrogenase

                                     

ⓘ Aminoadipate-semialdehyde dehydrogenase

This gene encodes a member of the non-ribosome peptide syntesase NRPS enzyme family. The encoded protein contains an AMP-binding domain, PP-binding phosphopantetheine, or pantetheine 4phosphate-binding domain and the Pyrrolo-quinoline quinon PQQ binding domain. The protein is expressed in several adult tissues.

                                     
  • enzymology, a L - aminoadipate - semialdehyde dehydrogenase EC 1.2.1.31 is an enzyme that catalyzes the chemical reaction L - 2 - aminoadipate 6 - semialdehyde NAD P
  • L - aminoadipate - semialdehyde dehydrogenase - phosphopantetheinyl transferase is an enzyme that in humans is encoded by the AASDHPPT gene. The protein encoded
  • survival, but necessary for long - term health. EC 1.2.1.31 L - aminoadipate - semialdehyde dehydrogenase Drain, Kelsey 12 February 2017 Natural Antioxidant
  • reduced by aminoadipate reductase via an acyl - enzyme intermediate to a semialdehyde Reaction with glutamate by one class of saccharopine dehydrogenase yields
  • glutamate - forming dehydrogenase aminoadipic semialdehyde - glutamic reductase, aminoadipate semialdehyde - glutamate reductase, aminoadipic semialdehyde - glutamate
  • Gene: AASS aminoadipate - semialdehyde synthase hyperlysinemia Genetics Home Reference. Retrieved 2017 - 03 - 04. Alpha - aminoadipic semialdehyde synthase
  • alpha - ketoglutarate Saccharopine dehydrogenase EC catalyses the condensation to of l - alpha - aminoadipate - delta - semialdehyde AASA with l - glutamate to give
  • catalysed by saccharopine dehydrogenases are: lysine alpha - ketoglutarate saccharopine glutamate 2 - aminoadipate 6 - semialdehyde Saccharopinuria high
  • Pyridoxine - dependent seizures caused by alpha amino adipic semialdehyde dehydrogenase deficiency: the first polish case with confirmed biochemical and