ⓘ PDSS1

                                     

ⓘ PDSS1

Decaprenyl-diphosphate synthase subunit 1 is an enzyme that in humans is encoded by the PDSS1 gene.

The protein encoded by this gene, the enzyme that adds prenyl side chain of coenzyme Q or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all TRANS-polyprenyl pyrophosphates from isopentyl diphosphate in the Assembly of polyisoprenoid side chains, the first step in the biosynthesis of coenzyme Q. may be a Protein indirectly linked to the inner mitochondrial membrane, though no transit peptide has been definitively identified to date.